BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide, BCKDHB)
Short Description: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform. [provided by RefSeq, Jul 2008].
More information related to gene BCKDHB.
More information related to gene BCKDHB.
Products related to BCKDHB Gene:
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54 results
ORF
Clon
Gateway Cloning Vector
pDONR223
Spectinomycin
unconjugated
Catalog No. ABIN5322702
$223.79
Plus shipping costs $50.00
2 μg
Shipping to:
United States
Delivery in 15 to 19 Business Days
ORF
PExp
Mammalian Expression Vector
pcDNA3.1+C-(K)-DYK
Ampicillin
CMV Promoter
DYKDDDDK Tag
Transient
- Type:
- ORF
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_000056
- Gene ID:
- 594 (Human, BCKDHB)
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pcDNA3.1+C-(K)-DYK
- Resistance Gene:
- Ampicillin
- Selection Marker:
- Neomycin
- Promoter:
- CMV Promoter
- Fusion Tag:
- DYKDDDDK Tag
- Expression:
- Transient, Stable
Catalog No. ABIN4932758
$319.00
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 6 to 9 Business Days
OriGene sc127427
cDNA
PExp
Mammalian Expression Vector
pCMV6-XL5
Ampicillin
Enhanced CMV Promoter
unconjugated
Transient
1
- Type:
- cDNA
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_183050,NP_898871
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-XL5
- Resistance Gene:
- Ampicillin
- Promoter:
- Enhanced CMV Promoter, T7 Promoter
- Expression:
- Transient
Catalog No. ABIN3382738
$452.43
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 4 to 9 Business Days
OriGene sc108972
cDNA
PExp
Mammalian Expression Vector
pCMV6-XL5
Ampicillin
Enhanced CMV Promoter
unconjugated
Transient
1
- Type:
- cDNA
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_000056,NP_000047
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-XL5
- Resistance Gene:
- Ampicillin
- Promoter:
- Enhanced CMV Promoter, T7 Promoter
- Expression:
- Transient
Catalog No. ABIN3382737
$452.43
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 4 to 9 Business Days
OriGene rc208059
ORF
PExp
Mammalian Expression Vector
pCMV6-Entry
Kanamycin
CMV Promoter
Myc-DYKDDDDK Tag
Transient
1
- Type:
- ORF
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_183050,NP_898871
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-Entry
- Resistance Gene:
- Kanamycin
- Promoter:
- CMV Promoter
- Fusion Tag:
- Myc-DYKDDDDK Tag
- Expression:
- Transient
Catalog No. ABIN5377538
$452.43
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 8 to 11 Business Days
OriGene rc218846
ORF
PExp
Mammalian Expression Vector
pCMV6-Entry
Kanamycin
CMV Promoter
Myc-DYKDDDDK Tag
Transient
1
- Type:
- ORF
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_000056,NP_000047
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-Entry
- Resistance Gene:
- Kanamycin
- Promoter:
- CMV Promoter
- Fusion Tag:
- Myc-DYKDDDDK Tag
- Expression:
- Transient
Catalog No. ABIN5377539
$452.43
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 8 to 11 Business Days
OriGene rg218846
ORF
PExp
Mammalian Expression Vector
pCMV6-AC-GFP
Ampicillin
CMV Promoter
GFP tag
Stable
1
- Type:
- ORF
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-AC-GFP
- Resistance Gene:
- Ampicillin
- Selection Marker:
- Neomycin
- Promoter:
- CMV Promoter
- Fusion Tag:
- GFP tag
- Expression:
- Stable, Transient
Catalog No. ABIN5377537
$484.11
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 8 to 11 Business Days
OriGene rn215528
cDNA
PExp
Mammalian Expression Vector
pCMV6-Entry
Kanamycin
Enhanced CMV Promoter
unconjugated
Transient
1
- Type:
- cDNA
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_019267,NP_062140
- Species:
- Rat
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-Entry
- Resistance Gene:
- Kanamycin
- Selection Marker:
- Neomycin
- Promoter:
- Enhanced CMV Promoter
- Expression:
- Transient
Catalog No. ABIN3374933
$497.97
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 31 to 32 Business Days
OriGene rr215528
ORF
PExp
Mammalian Expression Vector
pCMV6-Entry
Kanamycin
CMV Promoter
Myc-DYKDDDDK Tag
Transient
1
- Type:
- ORF
- Application:
- Protein Expression
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- NCBI Accession:
- NM_019267,NP_062140
- Species:
- Rat
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCMV6-Entry
- Resistance Gene:
- Kanamycin
- Promoter:
- CMV Promoter
- Fusion Tag:
- Myc-DYKDDDDK Tag
- Expression:
- Transient
Catalog No. ABIN5377540
$497.97
Plus shipping costs $50.00
10 μg
Shipping to:
United States
Delivery in 31 to 32 Business Days
OriGene sr410676
RNAi
BCKDHB
Species: Mouse
HPLC purified
- Application:
- RNA Interference
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide
- Species:
- Mouse
- Purification:
- HPLC purified
Catalog No. ABIN3273144
$512.82
Plus shipping costs $50.00
1 kit
Shipping to:
United States
Delivery in 16 to 17 Business Days
Synonyms and alternative names related to BCKDHB
- branched chain keto acid dehydrogenase E1, beta polypeptide (BCKDHB)
- branched chain keto acid dehydrogenase E1 subunit beta (BCKDHB)
- branched chain keto acid dehydrogenase E1, beta polypeptide (bckdhb)
- branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog (bckdhb.S)
- branched chain keto acid dehydrogenase E1 subunit beta (Bckdhb)
- branched chain ketoacid dehydrogenase E1, beta polypeptide (Bckdhb)
- BCKDHB
- dJ279A18.1
- E1B
- zgc:158777
Gene-IDs for different species
Protein level used designations for BCKDHB
- 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
- branched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)
- mitochondrial branched-chain alpha-keto acid dehydrogenase E1-beta subunit
- branched chain keto acid dehydrogenase E1, beta polypeptide
- branched chain keto acid dehydrogenase E1 beta polypeptide
- branched chain keto acid dehydrogenase E1 beta-like
- 2-oxoisovalerate dehydrogenase beta subunit
- BCKDE1B
- BCKDH E1-beta
- branched chain keto acid dehydrogenase E1 beta
- branched-chain alpha-keto acid dehydrogenase E1 component beta chain
- E1b-beta subunit of the branched-chain complex
- branched chain alpha-ketoacid dehydrogenase E1-beta subunit
Proteomics products related to BCKDHB Gene
Other products related to BCKDHB such as antibodies, ELISA kits and high-purity proteins are available on our partner website antibodies-online.com
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