BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide, BCKDHB)
Short Description: Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform. [provided by RefSeq, Jul 2008].
More information related to gene BCKDHB.
More information related to gene BCKDHB.
Products related to BCKDHB Gene:
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54 results
OriGene tl500196
shRNA
RNAi
Lentiviral Vector
pGFP-C-shLenti
Chloramphenicol
U6 Promoter
GFP tag
Transient
1
- Type:
- shRNA
- Application:
- RNA Interference
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- Species:
- Mouse
- Vector type:
- Lentiviral Vector
- Vector backbone:
- pGFP-C-shLenti
- Resistance Gene:
- Chloramphenicol
- Selection Marker:
- Puromycin
- Promoter:
- U6 Promoter
- Fusion Tag:
- GFP tag
- Expression:
- Transient, Stable
Catalog No. ABIN3701946
$1,002.87
Plus shipping costs $50.00
1 kit
Shipping to:
United States
Delivery in 16 to 17 Business Days
OriGene tl710276
shRNA
RNAi
Lentiviral Vector
pGFP-C-shLenti
Chloramphenicol
U6 Promoter
GFP tag
Transient
1
- Type:
- shRNA
- Application:
- RNA Interference
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- Species:
- Rat
- Vector type:
- Lentiviral Vector
- Vector backbone:
- pGFP-C-shLenti
- Resistance Gene:
- Chloramphenicol
- Selection Marker:
- Puromycin
- Promoter:
- U6 Promoter
- Fusion Tag:
- GFP tag
- Expression:
- Transient, Stable
Catalog No. ABIN3447557
$1,002.87
Plus shipping costs $50.00
1 kit
Shipping to:
United States
Delivery in 16 to 17 Business Days
OriGene kn408059
gRNA + Cas9
GEEN
Mammalian Expression Vector
pCas-Guide
Ampicillin
U6 Promoter
Myc-DYKDDDDK Tag
Transient
1
- Type:
- gRNA + Cas9
- Application:
- Genome Editing with Engineered Nucleases
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- Species:
- Human
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCas-Guide
- Resistance Gene:
- Ampicillin
- Promoter:
- U6 Promoter, Enhanced CMV Promoter
- Fusion Tag:
- Myc-DYKDDDDK Tag
- Expression:
- Transient
Catalog No. ABIN3247759
$1,640.43
Plus shipping costs $50.00
1 kit
Shipping to:
United States
Delivery in 21 to 22 Business Days
OriGene kn502091
gRNA + Cas9
GEEN
Mammalian Expression Vector
pCas-Guide
Ampicillin
U6 Promoter
Myc-DYKDDDDK Tag
Transient
1
- Type:
- gRNA + Cas9
- Application:
- Genome Editing with Engineered Nucleases
- Gene:
- Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB)
- Species:
- Mouse
- Vector type:
- Mammalian Expression Vector
- Vector backbone:
- pCas-Guide
- Resistance Gene:
- Ampicillin
- Promoter:
- U6 Promoter, Enhanced CMV Promoter
- Fusion Tag:
- Myc-DYKDDDDK Tag
- Expression:
- Transient
Catalog No. ABIN3247760
$1,640.43
Plus shipping costs $50.00
1 kit
Shipping to:
United States
Delivery in 21 to 22 Business Days
Synonyms and alternative names related to BCKDHB
- branched chain keto acid dehydrogenase E1, beta polypeptide (BCKDHB)
- branched chain keto acid dehydrogenase E1 subunit beta (BCKDHB)
- branched chain keto acid dehydrogenase E1, beta polypeptide (bckdhb)
- branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog (bckdhb.S)
- branched chain keto acid dehydrogenase E1 subunit beta (Bckdhb)
- branched chain ketoacid dehydrogenase E1, beta polypeptide (Bckdhb)
- BCKDHB
- dJ279A18.1
- E1B
- zgc:158777
Gene-IDs for different species
Protein level used designations for BCKDHB
- 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
- branched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)
- mitochondrial branched-chain alpha-keto acid dehydrogenase E1-beta subunit
- branched chain keto acid dehydrogenase E1, beta polypeptide
- branched chain keto acid dehydrogenase E1 beta polypeptide
- branched chain keto acid dehydrogenase E1 beta-like
- 2-oxoisovalerate dehydrogenase beta subunit
- BCKDE1B
- BCKDH E1-beta
- branched chain keto acid dehydrogenase E1 beta
- branched-chain alpha-keto acid dehydrogenase E1 component beta chain
- E1b-beta subunit of the branched-chain complex
- branched chain alpha-ketoacid dehydrogenase E1-beta subunit
Proteomics products related to BCKDHB Gene
Other products related to BCKDHB such as antibodies, ELISA kits and high-purity proteins are available on our partner website antibodies-online.com
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